: A 56-year-old woman with mixed connective tissue disease, who was on maintenance immunosuppression, developed asymptomatic left ventricular dysfunction, ventricular arrhythmia, and high troponin I. Heart catheterization showed normal coronaries and biopsy-proven, virus-negative lymphocytic myocarditis. A biopsy-guided immunosuppression upgrade effectively treated autoimmune myocarditis, which resulted in ventricular function recovery, resolution of arrhythmia, and of troponin release. (Level of Difficulty: Advanced.).

Biopsy-Proven Lymphocytic Myocarditis With Heart Failure in a Middle-Aged Female Patient With Mixed Connective Tissue Disease

Iliceto, Sabino;
2019-01-01

Abstract

: A 56-year-old woman with mixed connective tissue disease, who was on maintenance immunosuppression, developed asymptomatic left ventricular dysfunction, ventricular arrhythmia, and high troponin I. Heart catheterization showed normal coronaries and biopsy-proven, virus-negative lymphocytic myocarditis. A biopsy-guided immunosuppression upgrade effectively treated autoimmune myocarditis, which resulted in ventricular function recovery, resolution of arrhythmia, and of troponin release. (Level of Difficulty: Advanced.).
2019
AHA
anti-heart autoantibodies
AIDA
anti-intercalated autoantibodies
CMR
cardiac magnetic resonance
EMB
endomyocardial biopsy
HRCT
high-resolution chest computed tomography
LVEF
left ventricle ejection fraction
MCTD
mixed connective tissue disease
MMF
mycophenolate mofetil
MTP
methylprednisolone
SID
systemic immune mediated disease
autoimmune
cardiomyopathy
chronic heart failure
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/20.500.12572/37136
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